Coexistence of congenital cholesteatoma and non-neoplastic neuroectodermal remnants in the temporal bone:: Case report

Coskun U., Hidir Y., Karslioglu Y., Satar B.

JOURNAL OF INTERNATIONAL ADVANCED OTOLOGY, sa.3, ss.99-103, 2007 (Hakemli Dergi)

Özet

The most common location of congenital cholesteatoma, diagnosed these days at an increasing rate, is the anterosuperior quadrant of the tympanic cavity. Mastoid origin is rare, and neuroectodermal tissue remnant in the middle ear has not been reported to date. We discuss a patient whose congenital cholesteatoma was confined to the mastoid and coincided with the occurrence of non-neoplastic neuroectodermal remnant in the middle ear. The neuroectodermal remnant was accompanied by a blue tympanic membrane. The congenital cholesteatoma was asymptomatic at the time of initial diagnosis. Radiologic and clinical features of this very rare coincidence are discussed. This coexistence may help to support embryonicremnant theory in congenital cholesteatoma formation.